Which syndrome is characterized by a triad of anomalies including epibulbar dermoid and accessory auricular appendages?

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The correct answer is Goldenhar Syndrome, which is indeed characterized by a triad of anomalies, one of which includes epibulbar dermoids and accessory auricular appendages. Goldenhar Syndrome, also known as oculoauriculovertebral spectrum, represents a congenital condition that affects the development of the face and ears. This syndrome often presents with abnormal growths on the eyes (epibulbar dermoids), various defects of the ear (like accessory auricular appendages), and sometimes spinal anomalies. The combination of these features helps to clearly define the syndrome and differentiate it from others.

In contrast, Familial Dysautonomia primarily affects the autonomic nervous system and is not characterized by the specific physical abnormalities involving the eyes or ears. Holt-Oram Syndrome is associated with upper limb defects and congenital heart issues rather than the specific triad seen in Goldenhar. Kabuki Syndrome is identified by distinct facial features and skeletal abnormalities, but it does not feature the eye and ear anomalies seen in Goldenhar. This differentiation in symptomatology highlights why Goldenhar Syndrome is the correct answer.

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