Which syndrome is known for its association with anterior lenticonus without vision loss?

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Alport Syndrome is characterized by kidney disease, hearing loss, and eye abnormalities, one of which is anterior lenticonus. Anterior lenticonus is a conical protrusion of the anterior lens surface, and while it can influence vision, it does not always lead to vision loss for individuals affected by Alport Syndrome.

In understanding this syndrome's features, it is essential to note that the kidney issues associated with Alport Syndrome often manifest earlier than ocular complications, making the presence of anterior lenticonus notably significant during assessments despite it not always impacting visual acuity.

The other syndromes listed, while they may have their own unique traits and ocular findings, do not specifically highlight the association of anterior lenticonus without vision loss in the same manner that Alport Syndrome does. For instance, Wolfram Syndrome incorporates additional neurological symptoms, Brachio-oto-renal Syndrome focuses on branchial and ear anomalies, and Wiskott-Aldrich Syndrome is primarily an immunodeficiency disorder with hematological concerns, none of which emphasize anterior lenticonus as a key feature.

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